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Low activity of von Willebrand factor-cleaving protease is not restricted to patients suffering from thrombotic thrombocytopenic purpura.

作者信息

Loof A H, van Vliet H H, Kappers-Klunne M C

出版信息

Br J Haematol. 2001 Mar;112(4):1087-8. doi: 10.1046/j.1365-2141.2001.02622-5.x.

DOI:10.1046/j.1365-2141.2001.02622-5.x
PMID:11324640
Abstract
摘要

相似文献

1
Low activity of von Willebrand factor-cleaving protease is not restricted to patients suffering from thrombotic thrombocytopenic purpura.血管性血友病因子裂解蛋白酶活性降低并不局限于血栓性血小板减少性紫癜患者。
Br J Haematol. 2001 Mar;112(4):1087-8. doi: 10.1046/j.1365-2141.2001.02622-5.x.
2
von Willebrand factor-cleaving protease in thrombotic thrombocytopenic purpura and the hemolytic-uremic syndrome.血栓性血小板减少性紫癜和溶血尿毒综合征中的血管性血友病因子裂解蛋白酶
N Engl J Med. 1998 Nov 26;339(22):1578-84. doi: 10.1056/NEJM199811263392202.
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Deficient activity of von Willebrand factor-cleaving protease in thrombotic thrombocytopenic purpura.血栓性血小板减少性紫癜中血管性血友病因子裂解蛋白酶活性缺乏。
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Antibodies to von Willebrand factor-cleaving protease in acute thrombotic thrombocytopenic purpura.急性血栓性血小板减少性紫癜中针对血管性血友病因子裂解蛋白酶的抗体。
N Engl J Med. 1998 Nov 26;339(22):1585-94. doi: 10.1056/NEJM199811263392203.
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Immunotherapy for thrombotic thrombocytopenic purpura.血栓性血小板减少性紫癜的免疫疗法。
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[A woman suffering from systemic lupus erythematosus and acquired thrombotic thrombocytopenic purpura].一名患有系统性红斑狼疮和获得性血栓性血小板减少性紫癜的女性
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Thrombotic thrombocytopenic purpura attributable to von Willebrand factor-cleaving protease inhibitor in an 8-year-old boy.一名8岁男孩因血管性血友病因子裂解蛋白酶抑制剂导致血栓性血小板减少性紫癜。
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[Thrombotic thrombocytopenic purpura and von Willebrand factor- specific-cleaving enzyme].
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Deficiency of ADAMTS-13 in pediatric patients with severe sepsis and impact on in-hospital mortality.严重脓毒症患儿中ADAMTS - 13缺乏及其对院内死亡率的影响。
BMC Pediatr. 2013 Mar 28;13:44. doi: 10.1186/1471-2431-13-44.
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ADAMTS13 gene mutations in children with hemolytic uremic syndrome.儿童溶血尿毒综合征中 ADAMTS13 基因突变。
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ADAMTS-13 and Von Willebrand factor in relation to platelet response during plasma exchange in thrombotic thrombocytopenic purpura: a clue for disease mechanism?血栓性血小板减少性紫癜血浆置换过程中ADAMTS-13和血管性血友病因子与血小板反应的关系:疾病机制的线索?
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Semin Thromb Hemost. 2005 Dec;31(6):659-72. doi: 10.1055/s-2005-925472.