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ADAMTS-13 and Von Willebrand factor in relation to platelet response during plasma exchange in thrombotic thrombocytopenic purpura: a clue for disease mechanism?

作者信息

Kappers-Klunne M C, van Asten J G, van Vliet H H

出版信息

Ann Hematol. 2009 Oct;88(10):1025-8. doi: 10.1007/s00277-009-0709-7. Epub 2009 Feb 11.

DOI:10.1007/s00277-009-0709-7
PMID:19205653
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC2728906/
Abstract
摘要
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7543/2728906/3f8bb28629fc/277_2009_709_Fig1_HTML.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7543/2728906/3f8bb28629fc/277_2009_709_Fig1_HTML.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7543/2728906/3f8bb28629fc/277_2009_709_Fig1_HTML.jpg

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本文引用的文献

1
Thrombotic thrombocytopenic purpura in humans and mice.人类和小鼠中的血栓性血小板减少性紫癜。
Arterioscler Thromb Vasc Biol. 2007 Sep;27(9):1901-8. doi: 10.1161/ATVBAHA.107.145797. Epub 2007 May 24.
2
Size regulation of von Willebrand factor-mediated platelet thrombi by ADAMTS13 in flowing blood.在流动血液中,ADAMTS13对血管性血友病因子介导的血小板血栓的大小调节作用
Blood. 2006 Mar 1;107(5):1943-50. doi: 10.1182/blood-2005-07-2972. Epub 2005 Nov 17.
3
Platelet-derived VWF-cleaving metalloprotease ADAMTS-13.血小板衍生的血管性血友病因子裂解金属蛋白酶ADAMTS-13
J Thromb Haemost. 2005 Nov;3(11):2536-44. doi: 10.1111/j.1538-7836.2005.01561.x. Epub 2005 Sep 13.
4
Thrombotic thrombocytopenic purpura.血栓性血小板减少性紫癜
J Thromb Haemost. 2005 Aug;3(8):1663-75. doi: 10.1111/j.1538-7836.2005.01425.x.
5
Detection of von Willebrand factor-cleaving protease (ADAMTS-13) in human platelets.人血小板中血管性血友病因子裂解蛋白酶(ADAMTS-13)的检测
Biochem Biophys Res Commun. 2004 Jan 2;313(1):212-6. doi: 10.1016/j.bbrc.2003.11.111.
6
ADAMTS-13 rapidly cleaves newly secreted ultralarge von Willebrand factor multimers on the endothelial surface under flowing conditions.ADAMTS-13在流动条件下能迅速切割内皮表面新分泌的超大血管性血友病因子多聚体。
Blood. 2002 Dec 1;100(12):4033-9. doi: 10.1182/blood-2002-05-1401. Epub 2002 Jul 25.
7
Low activity of von Willebrand factor-cleaving protease is not restricted to patients suffering from thrombotic thrombocytopenic purpura.血管性血友病因子裂解蛋白酶活性降低并不局限于血栓性血小板减少性紫癜患者。
Br J Haematol. 2001 Mar;112(4):1087-8. doi: 10.1046/j.1365-2141.2001.02622-5.x.
8
Assay of von Willebrand factor (vWF)-cleaving protease based on decreased collagen binding affinity of degraded vWF: a tool for the diagnosis of thrombotic thrombocytopenic purpura (TTP).基于降解的血管性血友病因子(vWF)胶原结合亲和力降低的vWF裂解蛋白酶检测:一种用于诊断血栓性血小板减少性紫癜(TTP)的工具。
Thromb Haemost. 1999 Nov;82(5):1386-9.
9
Triplet structure of human von Willebrand factor.人血管性血友病因子的三联体结构
Biochem J. 1998 Apr 15;331 ( Pt 2)(Pt 2):483-8. doi: 10.1042/bj3310483.
10
Enzyme immunoassay for factor VIII-related antigen.因子VIII相关抗原的酶免疫测定法。
Clin Chem. 1982 Jun;28(6):1356-8.