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光疗联合苯巴比妥治疗Ⅱ型克里格勒-纳贾尔综合征并获得良好胎儿结局:一例病例报告

Phenobarbital following phototherapy for Crigler-Najjar syndrome type II with good fetal outcome: a case report.

作者信息

Ito T, Katagiri C, Ikeno S, Takahashi H, Nagata N, Terakawa N

机构信息

Department of Obstetrics and Gynecology, Hakuai Hospital, Yonago, Japan.

出版信息

J Obstet Gynaecol Res. 2001 Feb;27(1):33-5. doi: 10.1111/j.1447-0756.2001.tb01212.x.

Abstract

In the presence of severe hyperbilirubinemia in Crigler-Najjar syndrome Type II, a fetus is at risk for kernicterus. A 34-year-old woman, gravida 4, para 1, with Crigler-Najjar syndrome Type II was treated with phenobarbital administration following phototherapy during each of 2 pregnancies. Both infants were healthy and developed normally.

摘要

在II型克里格勒-纳贾尔综合征存在严重高胆红素血症的情况下,胎儿有发生核黄疸的风险。一名34岁、孕4产1的女性患有II型克里格勒-纳贾尔综合征,在两次怀孕期间每次接受光疗后均给予苯巴比妥治疗。两个婴儿均健康且发育正常。

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