Michailidis G D, Simpson J M, Tulloh R M, Economides D L
Fetal Medicine Unit, Department of Obstetrics and Gynaecology, Royal Free Hospital, London, UK.
Ultrasound Obstet Gynecol. 2001 May;17(5):449-52. doi: 10.1046/j.1469-0705.2001.00375.x.
Scimitar syndrome is a rare malformation of the arterial supply and venous drainage of the lung. We report the case of a fetus that presented with cardiac asymmetry and malposition of the fetal heart. Postnatally, scimitar syndrome was confirmed at cardiac catheterization. Retrospective reconstruction of three-dimensional power Doppler volumes, obtained during fetal life, allowed direct visualization of the abnormal aortopulmonary collateral vessel. This had not been seen on conventional scans. This case demonstrates many of the strengths of three-dimensional sonographic techniques for the delineation of complex vascular anatomy. It confirms that a prospective diagnosis of scimitar syndrome should be possible during fetal life.
弯刀综合征是一种罕见的肺动静脉发育畸形。我们报告了一例胎儿出现心脏不对称和心脏位置异常的病例。出生后，心脏导管检查确诊为弯刀综合征。对胎儿期获得的三维能量多普勒容积进行回顾性重建，可直接观察到异常的主肺动脉侧支血管，而这在传统扫描中未被发现。该病例展示了三维超声技术在描绘复杂血管解剖结构方面的诸多优势。这证实了在胎儿期应能够对弯刀综合征作出前瞻性诊断。
