Sapir S, Shapira J
Department of Pediatric Dentistry, the Hebrew University-Hadassah Faculty of Dental Medicine, Jerusalem, Israel.
Pediatr Dent. 2001 May-Jun;23(3):232-7.
Dentinogenesis imperfecta (DI) type 2 is a disease inherited in a simple autosomal dominant mode. As soon as the teeth erupt the parents may notice the problem and look for a pediatric dentist's advice and treatment. Early diagnosis and treatment of DI is recommended, as it may prevent or intercept deterioration of the teeth and occlusion and improve esthetics. The purpose of this article is to present the objectives, treatment options, and problems encountered in the treatment of DI in the early primary dentition. A two-stage treatment of a toddler under general anesthesia is described and discussed. This paper recommends for severe cases of DI two treatment stages performed under general anesthesia. Stage 1 is early (around age 18-20 months) and is directed to covering the incisors with composite restorations and the first primary molars with preformed crowns. Stage 2 (around age 28-30 months) seeks to protect the second primary molars with preformed crowns and cover the canines with composite restorations.
2型牙本质发育不全（DI）是一种以简单常染色体显性模式遗传的疾病。牙齿一旦萌出，家长可能就会注意到问题，并寻求儿童牙医的建议和治疗。建议对DI进行早期诊断和治疗，因为这可能预防或阻止牙齿和咬合的恶化，并改善美观。本文的目的是介绍乳牙列早期DI治疗的目标、治疗选择和遇到的问题。描述并讨论了在全身麻醉下对一名幼儿进行的两阶段治疗。本文建议对严重的DI病例在全身麻醉下进行两个治疗阶段。第一阶段较早（约18 - 20个月龄），旨在用复合树脂修复体覆盖切牙，用预成冠修复第一乳磨牙。第二阶段（约28 - 30个月龄）旨在用预成冠保护第二乳磨牙，并用复合树脂修复体覆盖尖牙。
