Murawa D, Nowakowski W, Sibilska E, Murawa P
I Oddział Chirurgii Onkologicznej Wielkopolskiego Centrum Onkologii w Poznaniu.
Pol Merkur Lekarski. 2001 Jun;10(60):460-1.
Authors present a rare case of primary lymphangiomyomatosis. Diagnosis was based on histopathological evaluation. Diagnostic difficulties were caused by lack of pathognomonic symptoms in clinical examination, ultrasonography and CT. The patient has been treated with hormonal medicines (Provera, Megace) since 1997. Now she is in a good condition, She hasn't got any symptoms of progression disease.
作者报告了一例罕见的原发性淋巴管平滑肌瘤病病例。诊断基于组织病理学评估。临床检查、超声检查和CT检查均缺乏特征性症状,导致诊断困难。自1997年以来,该患者一直接受激素药物(安宫黄体酮、甲地孕酮)治疗。目前她状况良好,没有任何疾病进展的症状。