Geha A S, Fry R D, Baue A E
J Thorac Cardiovasc Surg. 1975 Aug;70(2):223-8.
A 37-year-old man with the Marfan syndrome and chronic mitral regurgitation suffered an acute dissecting aneurysm of the ascending aorta with aortic regurgitation. Emergency replacement of the mitral valve, aortic valve, and ascending aorta was carried out, and the patient made an uneventful recovery. He is doing well 18 months after surgery. This is the first reported case of survival from such a procedure in the face of acute dissection with Marfan's syndrome. Indications for elective surgery are discussed and the uncertainties about the prognosis outlined. Continued reporting of the results and follow-up data are necessary for final assessment of the surgical treatment of the cardiovascular manifestations of this disease.
一名患有马凡综合征和慢性二尖瓣反流的37岁男性，发生了升主动脉急性夹层动脉瘤并伴有主动脉反流。紧急进行了二尖瓣、主动脉瓣和升主动脉置换术，患者术后恢复顺利。术后18个月他情况良好。这是首例报道的患有马凡综合征并面临急性夹层时经此手术存活的病例。文中讨论了择期手术的指征，并概述了预后的不确定性。持续报告结果和随访数据对于最终评估该疾病心血管表现的外科治疗是必要的。
