Takeda M, Kaneko Y, Ninomiya M, Kawauchi M, Kotsuka Y, Furuse A
Department of Cardiothoracic Surgery, Faculty of Medicine, University of Tokyo.
J Cardiol. 1997;29 Suppl 2:97-101.
A 28-year-old woman presented with Marfan syndrome combined with severe mitral regurgitation and annuloaortic ectasia. The ascending aorta was dilated to 48 mm in diameter without aortic regurgitation. Considering the increased operative risk due to complication with aortic dissection, simultaneous replacement of the mitral valve and aortic root were performed. Her postoperative course was uneventful. Several options of the surgical treatment for Marfan syndrome are discussed.
一名28岁女性因马凡综合征合并严重二尖瓣反流及主动脉瓣环扩张前来就诊。升主动脉直径扩张至48毫米,无主动脉反流。考虑到合并主动脉夹层会增加手术风险,遂同时进行二尖瓣和主动脉根部置换术。术后恢复顺利。文中讨论了马凡综合征手术治疗的几种选择。