Howlett S A, Shulman S T, Ayoub E M, Alexander R A, Donnelly W H, Cerda J J
Am J Dig Dis. 1975 Aug;20(8):790-5. doi: 10.1007/BF01070839.
A patient with cholangitis complicating congenital hepatic fibrosis is presented. In contrast to most other reported cases, many of whom have been treated surgically, this patient had a benign course. The likelihood that this complication of congenital hepatic fibrosis will respond to appropriate conservative therapy suggests that more aggressive forms of treatment should be reserved for those patients who fail to respond to medical management.
本文报告了一例患有胆管炎并伴有先天性肝纤维化的患者。与大多数其他已报道的病例不同，其中许多患者接受了手术治疗，而该患者病程呈良性。先天性肝纤维化的这种并发症对适当的保守治疗有反应，这表明对于那些对药物治疗无反应的患者，应保留更积极的治疗方式。
