Kostiainen S, Maamies T J
Ann Chir Gynaecol Fenn. 1975;64(1):40-3.
A 38 year old woman with congenital partial absence of the left pericardium is presented. The condition is fairly rare, usually diagnosed incidentally during intrathoracic operations or at autopsy. Eleven operatively corrected cases are reported in the literature. The present case was admitted because of transient attacks of chest pain, palpitation and dyspnoea. These attacks were brought on when she lay on her left side and were promptly relieved by a change of position. The chest radiograph revealed a prominence of the superior aspect of the left heart border and a slight laevo-position of the heart. A diagnostic pneumothorax on the left side confirmed the diagnosis of a pericardial defect. The defect was repaired by pericardioplasty. Operative correction of a partial left pericardial defect is indicated because of the danger of luxation of the heart out of the pericardium and sudden death. This has been reported, as well as a death caused by spreading of infection from the pleural cavity into the pericardium and heart.
本文报告了一名38岁先天性左心包部分缺如的女性患者。这种情况相当罕见，通常在开胸手术或尸检时偶然发现。文献报道了11例手术矫正病例。本例患者因胸痛、心悸和呼吸困难的短暂发作入院。这些发作在她左侧卧位时出现，改变体位后可迅速缓解。胸部X线片显示左心缘上部突出，心脏轻度左移。左侧诊断性气胸证实了心包缺损的诊断。通过心包成形术修复了缺损。由于存在心脏脱离心包的脱位风险和猝死风险，因此建议对部分左心包缺损进行手术矫正。这一点已有报道，此外还有因感染从胸腔蔓延至心包和心脏导致死亡的病例。
