Ramer M A, Lumerman H, Kopp W, Fisher K S, Cohen S A
Mount Sinai Medical Center, New York, USA.
Periodontal Clin Investig. 2001;23(1):31-5.
Epithelioid Hemangioendothelioma (EH) is a rare, low-grade malignant vascular tumor, first defined as a soft tissue tumor by Enzinger and Weiss in 1982. The tumor was later reported in virtually all sites, including liver, lung, brain, and bone. The epithelioid neoplastic cells are of endothelial origin, staining positive for Factor VIII and CD-34. In our review of EH of bone medline literature, and including the present case report, a total of 73 cases were found. Forty-one (56%) patients had multifocal bone involvement and thirty-two (44%) patients had solitary EH of bone. Resection was the primary recommended treatment. Visceral involvement appears to affect prognosis and survival adversely. We report a case of EH of the maxilla, which occurred in a 32-year-old male.
上皮样血管内皮瘤（EH）是一种罕见的低度恶性血管肿瘤，1982年由恩津格和魏斯首次定义为软组织肿瘤。该肿瘤后来在几乎所有部位都有报道，包括肝脏、肺、脑和骨骼。上皮样肿瘤细胞起源于内皮细胞，对因子VIII和CD-34染色呈阳性。在我们对骨上皮样血管内皮瘤的医学文献回顾中，包括本病例报告，共发现73例。41例（56%）患者有多发性骨受累，32例（44%）患者有孤立性骨上皮样血管内皮瘤。手术切除是主要推荐的治疗方法。内脏受累似乎对预后和生存有不利影响。我们报告一例上颌骨上皮样血管内皮瘤，发生于一名32岁男性。
