Charrier J B, Esnault O, Brette M D, Monteil J P
Department of Otorhinolaryngology and Maxillofacial Surgery, Faculty of Medicine Lariboisière Saint-Louis, University of Paris VII Hôpital Saint-Louis, Paris, France.
Br J Oral Maxillofac Surg. 2001 Oct;39(5):394-7. doi: 10.1054/bjom.2000.0635.
Alveolar soft-part sarcoma is a rare malignant tumour of uncertain histogenesis, the two main sites of which are the lower extremities in adults and the head and neck in children. We know of only three case reports of intraoral locations without tongue involvement. Here, we describe the first case of an alveolar soft-part sarcoma of the cheek which presented in a patient over 30 years old and had an extremely rapid and eventually fatal evolution. We have also reviewed hypotheses about its aetiology.
肺泡软组织肉瘤是一种组织发生不明的罕见恶性肿瘤，其两个主要发病部位在成人是下肢，在儿童是头颈部。我们仅知晓3例未累及舌部的口腔内发病的病例报告。在此，我们描述了首例发生于一名30多岁患者的颊部肺泡软组织肉瘤，其病情进展极快，最终导致死亡。我们还回顾了关于其病因的各种假说。
