Chu M K, Lee I H, Kim D I, Kim S M
Department of Neurology, Yonsei University College of Medicine, C.P.O. Box 8044, Seoul 120-752, Korea.
Yonsei Med J. 2001 Oct;42(5):566-70. doi: 10.3349/ymj.2001.42.5.566.
Progressive narrowing of distal carotid arteries and the development of compensatory fine networks are the characteristic findings of moyamoya disease. Cerebral infarction in moyamoya disease is due to a decreased blood flow and shows an uneven distribution in the distal bed of the anterior and middle cerebral arteries. The progression of disease in the posterior circulation follows that in the anterior circulation. Posterior circulation symptoms due to cerebral infarction usually occur in the advanced stage of the disease and follow the anterior circulation symptoms. We encountered an unusual case of moyamoya disease which initially presented with a transient visual field defect. One month later our patient developed blindness and her cerebral angiography showed advanced moyamoya disease.
颈内动脉末端渐进性狭窄以及代偿性精细血管网的形成是烟雾病的特征性表现。烟雾病中的脑梗死是由于血流减少所致，且在前、大脑中动脉远端供血区呈现分布不均。后循环的疾病进展与前循环一致。脑梗死所致的后循环症状通常出现在疾病晚期，且继发于前循环症状之后。我们遇到一例不寻常的烟雾病病例，最初表现为短暂性视野缺损。一个月后，患者失明，脑血管造影显示为晚期烟雾病。
