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僵腿综合征:病例报告

Stiff leg syndrome: case report.

作者信息

Gürol M E, Ertas M, Hanagasi H A, Sahin H A, Gürsoy G, Emre M

机构信息

Department of Neurology, Istanbul School of Medicine, University of Istanbul, Istanbul, Turkey.

出版信息

Mov Disord. 2001 Nov;16(6):1189-93. doi: 10.1002/mds.1224.

DOI:10.1002/mds.1224
PMID:11748762
Abstract

We report on a 28-year-old woman with insulin-resistant diabetes mellitus with a 5-year history of progressive stiffness and painful spasms of the right leg, exaggerated by sudden auditory and tactile stimuli or by emotional stress. There were no signs of truncal rigidity or exaggerated lumbar lordosis. Anti-glutamic acid decarboxylase antibodies were positive in her serum. She improved substantially with clonazepam 4 mg/day. She presented with electrophysiological findings not previously reported in stiff leg syndrome, which may suggest increased inhibition in the uninvolved upper extremities.

摘要

我们报告了一名28岁患有胰岛素抵抗型糖尿病的女性,她有5年右腿进行性僵硬和疼痛性痉挛的病史,突然的听觉和触觉刺激或情绪压力会使其加重。没有躯干僵硬或腰椎前凸加剧的迹象。她的血清中抗谷氨酸脱羧酶抗体呈阳性。她服用4毫克/天的氯硝西泮后有显著改善。她出现了僵硬腿综合征中以前未报道过的电生理结果,这可能表明未受累的上肢抑制作用增强。

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Stiff leg syndrome: case report.僵腿综合征:病例报告
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A Case of Anti-GAD 65 Autoimmune Encephalitis Associated with Focal Segmental Stiff-Person Syndrome.一例与局灶节段性僵人综合征相关的抗谷氨酸脱羧酶65自身免疫性脑炎病例。
Brain Sci. 2023 Feb 20;13(2):369. doi: 10.3390/brainsci13020369.
2
Effectiveness of Combined Immunoglobulin and Glucocorticoid Treatments in a Patient With Stiff Limb Syndrome: Case Report and Review of the Literature.联合免疫球蛋白和糖皮质激素治疗僵硬肢体综合征患者的疗效:病例报告及文献复习
Front Neurol. 2020 May 8;11:284. doi: 10.3389/fneur.2020.00284. eCollection 2020.
3
Autoimmune stiff person syndrome and related myelopathies: understanding of electrophysiological and immunological processes.
自身免疫性僵硬人综合征及相关脊髓病:电生理和免疫学过程的理解。
Muscle Nerve. 2012 May;45(5):623-34. doi: 10.1002/mus.23234.
4
Stiff limb syndrome: a case report.僵肢综合征:一例报告
Cases J. 2010 Feb 12;3:60. doi: 10.1186/1757-1626-3-60.