Yetiser S, Inal A, Taser M, Ozkaptan Y
Gulhane Medical School, Dept of ORL & HNS, Etlik 06018, Ankara, Turkey.
Rev Laryngol Otol Rhinol (Bord). 2001;122(3):195-200.
Relapsing Polychondritis (RP) is a rare disorder characterised by episodic inflammation of the cartilaginous structures. Differential diagnosis of this pathology is a challenging enigma since it appears only intermittently and none of the clinical features are pathognomonic, although most of the patients are usually referred to an ENT physician initially. The natural history of the disease is unpredictable. Initiating effective treatment sooner considerably reduces the rate of mortality. Patients with RP should be seen on a regular basis even if the patient is non-symptomatic. This study reports a retrospective analysis of the otolaryngological manifestations of 7 patients with RP as well as their long-term progress and reviews the symptomatology, histopathology, immunology and management.
复发性多软骨炎（RP）是一种罕见的疾病，其特征为软骨结构的发作性炎症。这种病症的鉴别诊断是一个具有挑战性的难题，因为它仅间歇性出现，且没有任何临床特征具有确诊意义，尽管大多数患者最初通常会被转诊至耳鼻喉科医生处。该疾病的自然病程不可预测。尽早开始有效治疗可显著降低死亡率。即使患者无症状，也应定期对RP患者进行检查。本研究报告了对7例RP患者的耳鼻喉科表现及其长期病程的回顾性分析，并对症状学、组织病理学、免疫学及治疗进行了综述。
