伴有关节病和骨质疏松症的非典型毛发红糠疹：一例随访15年的病例报告

Atypical pityriasis rubra pilaris associated with arthropathy and osteoporosis: a case report with 15-year follow-up.

作者信息

Behr Fiona D, Bangert Jerry L, Hansen Ronald C

机构信息

Section of Dermatology, University of Arizona College of Medicine, Tucson, Arizona, USA.

出版信息

Pediatr Dermatol. 2002 Jan-Feb;19(1):46-51. doi: 10.1046/j.1525-1470.2002.00004.x.

DOI:10.1046/j.1525-1470.2002.00004.x

PMID:11860571

Abstract

Pityriasis rubra pilaris (PRP) is an idiopathic papulosquamous disease that clinically presents with palmoplantar keratoderma and follicular hyperkeratotic papules that coalesce into scaly erythematous plaques. We report a unique case of atypical PRP beginning at 1 year of age with associated severe arthropathy and osteoporosis. We further discuss the clinical and histopathologic aspects of PRP, its possible etiology, and other associated conditions.

摘要

红皮病型毛发红糠疹（PRP）是一种特发性丘疹鳞屑性疾病，临床上表现为掌跖角化病和毛囊性角化过度丘疹，这些丘疹融合成鳞屑性红斑斑块。我们报告了一例罕见的非典型PRP病例，该病例始于1岁，伴有严重关节病和骨质疏松症。我们进一步讨论了PRP的临床和组织病理学方面、其可能的病因以及其他相关情况。