Tsuzuki Shinobu, Enver Tariq
Section of Gene Function and Regulation, Institute of Cancer Research, Chester Beatty Laboratories, London, United Kingdom.
Blood. 2002 May 1;99(9):3404-10. doi: 10.1182/blood.v99.9.3404.
Transcription factor GATA-2 is implicated in the survival and growth of multipotential progenitors. Here we report that the promyelocytic leukemia zinc finger (PLZF) protein can interact with GATA-2 and can modify its transactivation capacity. Fanconi anemia zinc finger (FAZF), a PLZF-homologous protein that has been variously described as ROG (repressor of GATA), and TZFP (testis zinc finger protein) also interact with GATA-2. The zinc finger region of GATA-2 is required for binding to PLZF and FAZF, but distinct interfaces on the PLZF and FAZF molecules mediate the interaction, suggesting that GATA-2 activity is controlled by these 2 homologous proteins through distinct mechanisms. GATA-2 can also physically associate with the PLZF-RARalpha fusion protein generated by the t(11;17) chromosomal translocation associated with acute promyelocytic leukemia (APL). Functional experiments showed that this interaction has the capacity to render GATA-dependent transcription responsive to treatment with a combination of all-trans retinoic acid and the histone deacetylase inhibitor trichostatin A (TSA). This combination of drugs has been shown to stimulate the terminal differentiation of leukemic t(11;17)-associated APL blasts, raising the possibility that GATA target genes may be involved in the molecular pathogenesis of APL.
转录因子GATA-2与多能祖细胞的存活和生长有关。在此我们报告,早幼粒细胞白血病锌指(PLZF)蛋白可与GATA-2相互作用,并可改变其反式激活能力。范可尼贫血锌指(FAZF),一种PLZF同源蛋白,曾被分别描述为ROG(GATA的阻遏物)和TZFP(睾丸锌指蛋白),也与GATA-2相互作用。GATA-2的锌指区域是与PLZF和FAZF结合所必需的,但PLZF和FAZF分子上不同的界面介导了这种相互作用,这表明GATA-2的活性由这两种同源蛋白通过不同机制控制。GATA-2还可与由与急性早幼粒细胞白血病(APL)相关的t(11;17)染色体易位产生的PLZF-RARα融合蛋白发生物理结合。功能实验表明,这种相互作用能够使GATA依赖的转录对全反式维甲酸和组蛋白去乙酰化酶抑制剂曲古抑菌素A(TSA)联合治疗产生反应。已证明这种药物组合可刺激与白血病t(11;17)相关的APL原始细胞的终末分化,这增加了GATA靶基因可能参与APL分子发病机制的可能性。