I型细胞病（粘脂贮积症II型）中培养的成纤维细胞分泌的异常溶酶体水解酶。 - Suppr

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Abnormal lysosomal hydrolases excreted by cultured fibroblasts in I-cell disease (mucolipidosis II).

作者信息

Vladutiu G D, Rattazzi M C

出版信息

Biochem Biophys Res Commun. 1975 Dec 1;67(3):956-64. doi: 10.1016/0006-291x(75)90768-8.

DOI:10.1016/0006-291x(75)90768-8

PMID:1201084

Abstract

摘要

相似文献

Abnormal lysosomal hydrolases excreted by cultured fibroblasts in I-cell disease (mucolipidosis II).

Biochem Biophys Res Commun. 1975 Dec 1;67(3):956-64. doi: 10.1016/0006-291x(75)90768-8.

Comparative enzymology of eleven acid hydrolases in cultured amniotic fluid cells, skin fibroblasts and embryonic lung fibroblasts, and the respective changes with the increasing age of the cell cultures.

Tohoku J Exp Med. 1985 Apr;145(4):437-45. doi: 10.1620/tjem.145.437.

I-cell disease (mucolipidosis II): resolution of N-acetyl-beta-D-glucosaminidase and alpha-L-fucosidase components by DEAE-cellulose chromatography.

Clin Sci Mol Med. 1975 Dec;49(6):543-50. doi: 10.1042/cs0490543.

Isoelectric focusing pattern of acid hydrolases in cultured fibroblasts, leucocytes and cell-free amniotic fluid.

Neuropadiatrie. 1977 Aug;8(3):238-52. doi: 10.1055/s-0028-1091520.

Acid hydrolases and other enzymes of rat and human mast cell secretory granules.

Kroc Found Ser. 1981;14:103-21.

Hormonal regulation of lysosomal hydrolases in the reproductive tract of the rabbit.

J Reprod Fertil. 1983 Mar;67(2):447-55. doi: 10.1530/jrf.0.0670447.

[The activity of various lysosomal acid hydrolases in the normal child. Premise to the biochemical study of cerebral lipidosis].

Minerva Pediatr. 1978 Feb 28;30(4):339-48.

Isoenzymes of four acid hydrolases in human kidney and urine.

Clin Chim Acta. 1974 Apr;52(2):239-43. doi: 10.1016/0009-8981(74)90216-2.

A new variant of mannosidosis with increased residual enzymatic activity and mild clinical manifestation.

Pediatr Res. 1978 Oct;12(10):1010-5. doi: 10.1203/00006450-197810000-00012.

Brain hexosaminidase and arylsulfatase isoenzymes in normal and vitamin E-deficient rats: an hypothesis for isoenzyme patterns in GM2 gangliosidoses and MLD.

Trans Am Neurol Assoc. 1974;99:140-3.

引用本文的文献

Lysosomal Storage Diseases-Regulating Neurodegeneration.

J Exp Neurosci. 2016 Apr 5;9(Suppl 2):81-91. doi: 10.4137/JEN.S25475. eCollection 2015.

Autophagy in lysosomal storage disorders.

Autophagy. 2012 May 1;8(5):719-30. doi: 10.4161/auto.19469.

Effects of di-isopropyl phosphorofluoridate on rat liver microsomal and lysosomal beta-glucuronidase.

Biochem J. 1977 Jun 15;164(3):549-56. doi: 10.1042/bj1640549.

Chick embryo fibroblasts produce two forms of hyaluronidase.

J Cell Biol. 1980 May;85(2):248-57. doi: 10.1083/jcb.85.2.248.

Influence of sialic acid on cell surface properties in I-cell disease fibroblasts.

In Vitro. 1981 Jul;17(7):588-92. doi: 10.1007/BF02618456.

Multiple molecular forms of lysosomal enzymes in mucolipidosis II.

Hum Genet. 1981;58(3):317-21. doi: 10.1007/BF00294931.

Compartmental distribution of beta-hexosaminidase isoenzymes in I-cell fibroblasts.

Biochem J. 1981 Jun 15;196(3):657-62. doi: 10.1042/bj1960657.

The effect of monensin on beta-hexosaminidase transport in normal and I-cell fibroblasts.

Biochem J. 1980 Dec 15;192(3):813-20. doi: 10.1042/bj1920813.

The effect of chloroquine on the distribution of newly synthesized and old beta-hexosaminidase in fibroblasts.

Biochem J. 1982 Dec 15;208(3):559-66. doi: 10.1042/bj2080559.

Correction of I-cell defect by hybridization with lysosomal enzyme deficient human fibroblasts.

Am J Hum Genet. 1980 Jul;32(4):519-28.

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Abnormal lysosomal hydrolases excreted by cultured fibroblasts in I-cell disease (mucolipidosis II).

作者信息

Vladutiu G D, Rattazzi M C

出版信息

Biochem Biophys Res Commun. 1975 Dec 1;67(3):956-64. doi: 10.1016/0006-291x(75)90768-8.

DOI:10.1016/0006-291x(75)90768-8

PMID:1201084

Abstract

摘要

相似文献

Abnormal lysosomal hydrolases excreted by cultured fibroblasts in I-cell disease (mucolipidosis II).

Biochem Biophys Res Commun. 1975 Dec 1;67(3):956-64. doi: 10.1016/0006-291x(75)90768-8.

Tohoku J Exp Med. 1985 Apr;145(4):437-45. doi: 10.1620/tjem.145.437.

I-cell disease (mucolipidosis II): resolution of N-acetyl-beta-D-glucosaminidase and alpha-L-fucosidase components by DEAE-cellulose chromatography.

Clin Sci Mol Med. 1975 Dec;49(6):543-50. doi: 10.1042/cs0490543.

Isoelectric focusing pattern of acid hydrolases in cultured fibroblasts, leucocytes and cell-free amniotic fluid.

Neuropadiatrie. 1977 Aug;8(3):238-52. doi: 10.1055/s-0028-1091520.

Acid hydrolases and other enzymes of rat and human mast cell secretory granules.

Kroc Found Ser. 1981;14:103-21.

Hormonal regulation of lysosomal hydrolases in the reproductive tract of the rabbit.

J Reprod Fertil. 1983 Mar;67(2):447-55. doi: 10.1530/jrf.0.0670447.

[The activity of various lysosomal acid hydrolases in the normal child. Premise to the biochemical study of cerebral lipidosis].

Minerva Pediatr. 1978 Feb 28;30(4):339-48.

Isoenzymes of four acid hydrolases in human kidney and urine.

Clin Chim Acta. 1974 Apr;52(2):239-43. doi: 10.1016/0009-8981(74)90216-2.

A new variant of mannosidosis with increased residual enzymatic activity and mild clinical manifestation.

Pediatr Res. 1978 Oct;12(10):1010-5. doi: 10.1203/00006450-197810000-00012.

Brain hexosaminidase and arylsulfatase isoenzymes in normal and vitamin E-deficient rats: an hypothesis for isoenzyme patterns in GM2 gangliosidoses and MLD.

Trans Am Neurol Assoc. 1974;99:140-3.

引用本文的文献

Lysosomal Storage Diseases-Regulating Neurodegeneration.

J Exp Neurosci. 2016 Apr 5;9(Suppl 2):81-91. doi: 10.4137/JEN.S25475. eCollection 2015.

Autophagy in lysosomal storage disorders.

Autophagy. 2012 May 1;8(5):719-30. doi: 10.4161/auto.19469.

Effects of di-isopropyl phosphorofluoridate on rat liver microsomal and lysosomal beta-glucuronidase.

Biochem J. 1977 Jun 15;164(3):549-56. doi: 10.1042/bj1640549.

Chick embryo fibroblasts produce two forms of hyaluronidase.

J Cell Biol. 1980 May;85(2):248-57. doi: 10.1083/jcb.85.2.248.

Influence of sialic acid on cell surface properties in I-cell disease fibroblasts.

In Vitro. 1981 Jul;17(7):588-92. doi: 10.1007/BF02618456.

Multiple molecular forms of lysosomal enzymes in mucolipidosis II.

Hum Genet. 1981;58(3):317-21. doi: 10.1007/BF00294931.

Compartmental distribution of beta-hexosaminidase isoenzymes in I-cell fibroblasts.

Biochem J. 1981 Jun 15;196(3):657-62. doi: 10.1042/bj1960657.

The effect of monensin on beta-hexosaminidase transport in normal and I-cell fibroblasts.

Biochem J. 1980 Dec 15;192(3):813-20. doi: 10.1042/bj1920813.

The effect of chloroquine on the distribution of newly synthesized and old beta-hexosaminidase in fibroblasts.

Biochem J. 1982 Dec 15;208(3):559-66. doi: 10.1042/bj2080559.

Correction of I-cell defect by hybridization with lysosomal enzyme deficient human fibroblasts.

Am J Hum Genet. 1980 Jul;32(4):519-28.