黏脂贮积症II中溶酶体酶的多种分子形式。 - Suppr

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Multiple molecular forms of lysosomal enzymes in mucolipidosis II.

作者信息

Farrell D F, MacMartin M P

出版信息

Hum Genet. 1981;58(3):317-21. doi: 10.1007/BF00294931.

DOI:10.1007/BF00294931

PMID:7327554

Abstract

摘要

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Multiple molecular forms of lysosomal enzymes in mucolipidosis II.黏脂贮积症II中溶酶体酶的多种分子形式。

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Mutant enzymatic and cytological phenotypes in cultured human fibroblasts.培养的人成纤维细胞中的突变酶学和细胞学表型。

Science. 1967 Aug 18;157(3790):804-6. doi: 10.1126/science.157.3790.804.

Protein measurement with the Folin phenol reagent.使用福林酚试剂进行蛋白质测定。

J Biol Chem. 1951 Nov;193(1):265-75.

Biosynthetic intermediates of beta-glucuronidase contain high mannose oligosaccharides with blocked phosphate residues.β-葡萄糖醛酸酶的生物合成中间体含有带有封闭磷酸残基的高甘露糖寡糖。

J Biol Chem. 1980 Jul 25;255(14):6633-9.

Effect of tunicamycin on the biosynthesis of the major human red cell sialoglycoprotein, glycophorin A, in the leukemia cell line K562.衣霉素对白血病细胞系K562中主要人类红细胞唾液糖蛋白血型糖蛋白A生物合成的影响。

J Biol Chem. 1980 Mar 10;255(5):2169-75.

Effects of tunicamycin on the biosynthesis of procollagen by human fibroblasts.衣霉素对人成纤维细胞前胶原生物合成的影响。

J Biol Chem. 1980 Jan 10;255(1):121-8.

Biosynthesis of lysosomal enzymes in fibroblasts. Phosphorylation of mannose residues.成纤维细胞中溶酶体酶的生物合成。甘露糖残基的磷酸化。

J Biol Chem. 1980 May 25;255(10):4946-50.

Enzymatic phosphorylation of lysosomal enzymes in the presence of UDP-N-acetylglucosamine. Absence of the activity in I-cell fibroblasts.在UDP-N-乙酰葡糖胺存在的情况下溶酶体酶的酶促磷酸化。I型细胞成纤维细胞中缺乏该活性。

Biochem Biophys Res Commun. 1981 Feb 12;98(3):761-7. doi: 10.1016/0006-291x(81)91177-3.

Catabolism of desialylated ceruloplasmin in the liver.肝脏中去唾液酸铜蓝蛋白的分解代谢

J Biol Chem. 1970 Nov 10;245(21):5833-7.

Globoid cell (Krabbe's) leukodystrophy: heterozygote detection in cultured skin fibroblasts.球状细胞（克拉伯氏）脑白质营养不良：培养的皮肤成纤维细胞中杂合子的检测

Am J Hum Genet. 1973 Nov;25(6):604-9.

Physicochemical modifications of lysosomal hydrolases during intracellular transport.溶酶体水解酶在细胞内运输过程中的物理化学修饰。

Biochem J. 1973 Feb;132(2):267-82. doi: 10.1042/bj1320267.

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