Holbach Leonard M, Colombo Fernando, Schlötzer-Schrehardt Ursula, Kirchner Thomas
Department of Ophthalmology & Eye Hospital, University of Erlangen-Nürnberg, Germany.
Orbit. 2002 Mar;21(1):49-54. doi: 10.1076/orbi.21.1.49.2601.
A 54-year-old white male patient presented with a painless, slowly progressive proptosis and downward displacement of his right eye. He had been treated for Hodgkin's disease 20 years earlier. MRI revealed a well-circumscribed retro- and suprabulbar mass measuring 24 mm in its maximal diameter. The mass was isointense with brain on T1-weighted images, displayed a low signal on T2-weighted images and showed postcontrast enhancement. The tumor was removed in its entirety via an anterior orbitotomy. Histopathologic, immunohistochemical and ultrastructural studies revealed a solitary fibrous tumor. Both immunohistochemical and electron microscopic findings were essential in differentiating this entity from other similar soft-tissue lesions. Only 11 other cases of orbital solitary fibrous tumor have been reported in the literature. To our knowledge, this is the first one presenting after Hodgkin's disease.