Partial anomalous pulmonary venous connection of singular form.

We have recently experienced a rare case of partial anomalous pulmonary venous connection, in a 3-year-old female. The case was diagnosed preoperatively as anomalous left superior pulmonary venous connection with atrial septal defect. Surgery, however, revealed that only the right superior pulmonary vein returned to the left atrium, while the other three pulmonary veins returned to the coronary sinus or innominate vein. No associated atrial septal defect was found. An enlarged coronary sinus was observed. In the present case, three of the four pulmonary veins were found to have anomalous connections, and were hemodynamically close to being total anomalous pulmonary venous connection. We performed unique radical surgery using autologous tissue for multiple anomalous pulmonary venous connections and here report the results, with a short discussion of the literature.