Quero Jiménez M, Burgueros Valero M, Herraiz Sarachaga L, Nieto Curatero J A, Acerete Guillén F
An Esp Pediatr. 1975 Nov-Dec;8(6):651-62.
Clinical and pathological findings are reported in 3 cases of cardiac tumors involving the ventricular septum and free walls. In 2 cases death occurred at ages 4 hours and 3 1/2 years and the pathological study revealed the presence of rhabdomyomas in the heart and tuberous sclerosis in the brain. The cardiac involvement was much more pronounced in the newborn infant than in the 3 1/2-year-old boy. The remaining patient, is a 6-month-old infant who is still alive. An angiocardiographic study performed at age 1 1/2-months revealed the presence of multple filling defects which were localized in the ventricular septum and in the left ventricular free wall. The angiocardiography was indicated on the basis of a previous clinical situation of severe heart failure which had been difficult to bring under control. A discussion is also presented dealing with the most characteristic clinical features of cardiac tumors in infants and children.
报告了3例累及室间隔和游离壁的心脏肿瘤的临床和病理结果。其中2例分别在出生4小时和3岁半时死亡，病理研究显示心脏存在横纹肌瘤，脑部存在结节性硬化症。新生儿心脏受累比3岁半男孩更明显。其余1例患者为6个月大婴儿，仍存活。1个半月大时进行的心血管造影研究显示，在室间隔和左心室游离壁存在多个充盈缺损。进行心血管造影是基于先前严重心力衰竭的临床情况难以控制。本文还讨论了婴幼儿心脏肿瘤最具特征性的临床特征。
