General and dental characteristics of Bloch-Sulzberger syndrome. Review of literature and presentation of a case report.

A case report of Bloch-Sulzberger Incontinentia Pigmenti is presented, in which the dental symptoms are considered as a base, not just for a review of this disorder within the scope of Integrated Paediatric Dentistry, but also in order to establish an adequate dental treatment for the affected children. There should be interdisciplinary coordination, leading to better treatment and therefore an improved quality of life for these patients.