Kumashiro Yuji, Kasahara Mureo, Nomoto Kazuhiro, Kawai Masaru, Sasaki Katsuya, Kiuchi Tetsuya, Tanaka Koichi
Department of Transplantation and Immunology, Kyoto University, Faculty of Medicine, Kyoto, Japan.
Liver Transpl. 2002 Aug;8(8):721-4. doi: 10.1053/jlts.2002.33689.
We present a case of a giant hepatic hemangioma with Kasabach-Merritt syndrome, which was cured by living donor liver transplantation. A 48-year-old woman complained of abdominal fullness and appetite loss. The laboratory data showed disseminated intravascular coagulation and a morphologic evaluation revealed a giant hepatic hemangioma involving both lobes of the liver. Living donor liver transplantation was indicated for Kasabach-Merritt syndrome and an unresectable liver tumor. A posterior segment graft was used because the remnant liver volume of the donor might have been too small to sustain the liver function of the donor. The postoperative course was uneventful, and the recipient was discharged from hospital on day 15 after the transplantation without complications.
我们报告一例伴有卡萨巴赫-梅里特综合征的巨大肝血管瘤患者,该患者通过活体肝移植治愈。一名48岁女性主诉腹部胀满和食欲减退。实验室检查显示弥散性血管内凝血,形态学评估发现一个累及肝脏两叶的巨大肝血管瘤。因卡萨巴赫-梅里特综合征和不可切除的肝脏肿瘤,该患者接受了活体肝移植。由于供体的残余肝体积可能过小,无法维持供体的肝功能,因此使用了肝右后叶移植物。术后过程顺利,受者在移植后第15天出院,无并发症。