Mahendran C, Singh P, Mani N B S, Jindal S K
Department of Pulmonary Medicine, Postgraduate Institute of Medical Education and Research, Chandigarh, India.
Respiration. 2002;69(4):355-8. doi: 10.1159/000063262.
Pulmonary artery aneurysm (PAA) secondary to Behçet's disease (BD) is a rare condition. The commonest presentation is hemoptysis, which can be fatal. Though the classical triad of recurrent oral and genital ulcers and relapsing iritis is present in most patients of BD, isolated pulmonary artery involvement termed as incomplete BD has been reported. Prompt diagnosis and immunosuppressive therapy can cause regression of aneurysm and prevent fatal hemoptysis. We report a case of PAA due to BD who presented with hemoptysis and responded to steroid therapy.
白塞病（BD）继发的肺动脉瘤（PAA）是一种罕见疾病。最常见的表现是咯血，这可能是致命的。尽管大多数BD患者存在复发性口腔和生殖器溃疡以及复发性虹膜炎这一经典三联征，但也有报道称存在孤立性肺动脉受累，即不完全型BD。及时诊断和免疫抑制治疗可使动脉瘤消退并预防致命性咯血。我们报告一例因BD导致的PAA患者，该患者表现为咯血且对类固醇治疗有反应。
