Kage Hidenori, Goto Yasushi, Amano Yosuke, Makita Kosuke, Isago Hideaki, Kobayashi Kouichi, Narumoto Osamu, Okudaira Reiko, Tanaka Goh, Takami Kazutaka, Ohishi Nobuya, Nagase Takahide
Department of Respiratory Medicine, The University of Tokyo, Japan.
Intern Med. 2016;55(22):3337-3340. doi: 10.2169/internalmedicine.55.6852. Epub 2016 Nov 15.
We herein describe a patient with Behçet's disease in whom we followed the development and resolution of pulmonary artery aneurysms. He presented with intermittent hemoptysis, pulmonary thromboembolism was initially diagnosed, and anticoagulant therapy was started. Over the next several months, the expansion of pulmonary arteries was noted. Five months after his initial admission, he was readmitted for massive hemoptysis, and further examinations revealed that he had Behçet's disease. Corticosteroids and intravenous cyclophosphamide were started. Over the next five months, the pulmonary artery aneurysms and thrombosis resolved. The development of pulmonary artery aneurysms led to the diagnosis of Behçet's disease, and they resolved after immunosuppressive therapy.
我们在此描述一名患有白塞病的患者，我们跟踪观察了其肺动脉瘤的发展及消退情况。他最初表现为间歇性咯血，最初被诊断为肺血栓栓塞，并开始了抗凝治疗。在接下来的几个月里，发现肺动脉有扩张。首次入院五个月后，他因大量咯血再次入院，进一步检查发现他患有白塞病。开始使用皮质类固醇和静脉注射环磷酰胺。在接下来的五个月里，肺动脉瘤和血栓消失。肺动脉瘤的出现导致了白塞病的诊断，并且在免疫抑制治疗后消失。
