Nezelof C, Laurent M, Imbert M C, Jaubert F
Arch Fr Pediatr. 1975 Nov;32(9):815-34.
The multilocular renal cystadenoma is a benign, rather uncommon tumor occurring in childhood (one case for 40 Wilms tumors). The clinical pathological study of five cases and the review of cases published in the literature show that this tumor, like all cystadenomata, is constituted by isolated cysts lined with cubic epithelium and inserted into each other. These cysts are included into mature mesenchymatous tissue. The renal cystadenoma appears as a large, regular, spheric mass, sharply demarcated from the pelvic cavities and renal parenchyma. Its volume is the main clinical sign. Occasionally, angiographic and echographic investigations may provide additional useful data. In some cases, the renal cystadenoma may be difficult to distinguish from a well differenciated cystic nephroblastoma. The differential features are emphasized and discussed. The renal cystadenoma must be regarded as a hamartoma developed from some metanephrogenic blastematous areas excluded from the normal embryogenetic process. The term of renal cystadenoma emphasizes the neoplastic nature and the macroscopic appearance of this tumor and must be preferred to designate this lesion.
多房性肾囊肿腺瘤是一种良性但相当罕见的肿瘤，发生于儿童期（每40例肾母细胞瘤中有1例）。对5例病例的临床病理研究以及对文献中已发表病例的回顾表明，这种肿瘤与所有囊腺瘤一样，由内衬立方上皮且相互嵌合的孤立囊肿构成。这些囊肿包埋于成熟的间充质组织中。肾囊肿腺瘤表现为一个大的、规则的球形肿块，与肾盂和肾实质界限清晰。其体积是主要的临床体征。偶尔，血管造影和超声检查可能提供额外有用的数据。在某些情况下，肾囊肿腺瘤可能难以与分化良好的囊性肾母细胞瘤相鉴别。文中强调并讨论了鉴别特征。肾囊肿腺瘤必须被视为一种由正常胚胎发生过程中排除的某些后肾胚芽组织区域发展而来的错构瘤。肾囊肿腺瘤这一术语强调了该肿瘤的肿瘤性质和宏观外观，在命名这种病变时应优先选用。
