Rosch R, Junge K, Töns C, Chalabi K, Klosterhalfen B, Schumpelick V
Chirurgische Klinik und Poliklinik der RWTH Aachen, Germany.
Chirurg. 2002 Sep;73(9):950-3. doi: 10.1007/s00104-002-0510-9.
Primary vascular leiomyosarcomas of the great vessels are rare and the most common localization is the inferior vena cava. Due to nonspecific clinical signs, diagnosis is often made during operation or autopsy. At present, a radical tumor resection is the first choice of treatment. This is a case report of a 49-year-old woman who suffered from abdominal pain for 10 years because of a weakly malignant leiomyosarcoma of the inferior vena cava. A radical tumor resection and reconstruction with a prosthetic vascular graft were performed. Diagnosis, therapy, and prognosis are discussed.
大血管原发性血管平滑肌肉瘤罕见,最常见的部位是下腔静脉。由于临床症状不具特异性,诊断往往在手术或尸检时作出。目前,根治性肿瘤切除术是首选治疗方法。本文报告一例49岁女性,因下腔静脉低度恶性平滑肌肉瘤腹痛10年。行根治性肿瘤切除及人工血管移植重建术。并对诊断、治疗及预后进行了讨论。