Drukker Lior, Alberton Joseph, Reissman Petachia
Vascular and General Surgery Department, Shaare Zedek Medical Center, Hadassah-Hebrew University School of Medicine, Jerusalem, Israel.
Vasc Endovascular Surg. 2012 Nov;46(8):688-90. doi: 10.1177/1538574412460102. Epub 2012 Sep 13.
Leiomyosarcoma of the inferior vena cava (IVC) is a rare tumor of mesenchymal origin, occurring most frequently in middle-aged women. Insidious complaints delay diagnosis, prognosis is poor, and the only curative modality remains an aggressive surgical resection yielding clear margins of disease. Commonly, radical tumor excision mandates caval repair or reconstruction, with significant related morbidity and mortality. We present a case of a 50-year-old woman with a leiomyosarcoma arising from the lower segment of the IVC, managed by surgical en-bloc resection of the tumor and IVC segment without further caval repair or reconstruction. During 14 months of follow-up the patient is well, had not had any complications, and is disease free.
下腔静脉平滑肌肉瘤是一种罕见的间叶源性肿瘤，最常见于中年女性。隐匿性症状延误诊断，预后较差，唯一的治愈方式仍是进行能获得清晰切缘的积极手术切除。通常，根治性肿瘤切除需要进行腔静脉修复或重建，这会带来显著的相关发病率和死亡率。我们报告一例50岁女性患者，其下腔静脉下段发生平滑肌肉瘤，通过手术整块切除肿瘤及下腔静脉节段，无需进一步的腔静脉修复或重建。在14个月的随访期间，患者情况良好，未出现任何并发症，且无疾病复发。
