Hardy Thomas G, McNab Alan A
Orbital, Plastic and Lacrimal Unit, Royal Victorian Eye and Ear Hospital, Melbourne, Australia.
Ophthalmic Plast Reconstr Surg. 2002 Sep;18(5):388-90. doi: 10.1097/00002341-200209000-00014.
To describe a case of familial Paget disease of bone associated with bilateral enophthalmos and mild exposure keratopathy.
Case report and literature review.
A 71-year-old woman with familial Paget disease of bone had a long history of "receding eyes," headaches, and moderately dry eyes. She had bilateral enophthalmos with mild exposure keratopathy. Radiologic and endocrinologic investigation confirmed Paget disease of bone affecting the skull.
Enophthalmos in association with Paget disease of bone is rare and is likely to result from differential expansion of the cranium compared with the orbital bones.
描述一例与双侧眼球内陷及轻度暴露性角膜病变相关的家族性骨佩吉特病病例。
病例报告及文献复习。
一名患有家族性骨佩吉特病的71岁女性有“眼球后缩”、头痛及中度干眼的长期病史。她患有双侧眼球内陷及轻度暴露性角膜病变。影像学和内分泌学检查证实颅骨患有骨佩吉特病。
骨佩吉特病相关的眼球内陷罕见，可能是由于颅骨与眶骨的差异性扩张所致。
