Chidgey M
Division of Medical Sciences, University of Birmingham, Clinical Research Block, Queen Elizabeth Hospital, Birmingham B15 2TH, UK.
Histol Histopathol. 2002 Oct;17(4):1179-92. doi: 10.14670/HH-17.1179.
Desmosomes play a critical role in the maintenance of normal tissue architecture. Skin blistering can occur when desmosomal adhesion is compromised by antibodies in autoimmune diseases such as pemphigus. Inherited mutations in genes encoding desmosomal constituents can adversely affect the skin, and result in heart abnormalities. Desmosomes may have a tumour suppressor function: expression of desmosomal components is reduced in some human cancers, and desmosomal cadherins have the capacity to suppress the invasiveness of cells in culture. Transgenic animal research has provided important insights into the role of these junctions in normal epithelial morphogenesis and disease.
桥粒在维持正常组织结构中起着关键作用。在自身免疫性疾病(如天疱疮)中,当桥粒黏附因抗体而受损时,皮肤会出现水疱。编码桥粒成分的基因发生遗传性突变会对皮肤产生不利影响,并导致心脏异常。桥粒可能具有肿瘤抑制功能:在某些人类癌症中,桥粒成分的表达会降低,并且桥粒钙黏蛋白具有抑制培养细胞侵袭性的能力。转基因动物研究为这些连接在正常上皮形态发生和疾病中的作用提供了重要见解。