Rongioletti F, Cattarini G, Romanelli P
Department of Endocrinological and Metabolic Diseases, Section of Dermatology, University of Genoa, Italy.
Clin Exp Dermatol. 2002 Sep;27(6):445-7. doi: 10.1046/j.1365-2230.2002.01027.x.
Steatocystoma multiplex is a rare, autosomal dominant condition characterized by multiple cysts, usually arising on the trunk and proximal extremities at puberty. We present two unrelated women with sporadic steatocystoma multiplex strictly confined to the vulva and arising at an older age. These cases represent an unusual localized form of the disorder.
多发性皮脂腺囊肿是一种罕见的常染色体显性遗传病，其特征为多个囊肿，通常在青春期出现在躯干和近端肢体。我们报告了两名不相关的女性，她们患有散发性多发性皮脂腺囊肿，且囊肿仅局限于外阴，发病年龄较大。这些病例代表了该疾病一种不寻常的局限性形式。
