Puertas I, García-Soldevilla M A, Jiménez-Jiménez F J, Cabrera-Valdivia F, Jabbour T, García-Albea E
Seccion de Neurología, Hospital Universitario Principe de Asturias, Alcalá de Henares, España.
Rev Neurol. 2002;35(5):430-3.
The main clinical feature of the opercular syndrome (Foix Chavany Marie) is the automatic voluntary dissociation of the facio glosso pharyngeal movements (that is, the alteration of voluntary motility with preservation of authomatic movements). Less frequently, it is presented with movement disorders as dystonia.
We report a male patient aged 40 years who developed a biopercular syndrome of vascular etiology (confirmed by neuroimaging), in the context or a clinical picture of global hipoxemia, for which the most outstanding clinical manifestation was the presence of dystonic posturing.
Although dystonia is usually related with damage or dysfunction of the basal ganglia or thalamus, in some case it can be caused by lesions in other locations, such as in some patients with biopercular syndrome as in the present case
opercular综合征(福-夏-马综合征)的主要临床特征是面舌咽运动的自动与随意分离(即随意运动障碍而自动运动保留)。较少见的情况下,会表现为如肌张力障碍等运动障碍。
我们报告一名40岁男性患者,在全身性低氧血症的临床背景下,出现了血管性病因的双侧opercular综合征(经神经影像学证实),其最突出的临床表现是肌张力障碍姿势。
虽然肌张力障碍通常与基底神经节或丘脑的损伤或功能障碍有关,但在某些情况下,它可能由其他部位的病变引起,如本例双侧opercular综合征患者。