Rivas Katherine, Pan Jie, Chen Angela, Gutiérrez Bailey, Julayanont Parunyou
School of Medical Sciences, National Autonomous University of Honduras, Tegucigalpa, Honduras.
Department of Neurology, Texas Tech University Health Sciences Center School of Medicine, Lubbock, Texas.
Proc (Bayl Univ Med Cent). 2021 Feb 2;34(3):389-390. doi: 10.1080/08998280.2021.1878976.
Foix-Chavany-Marie syndrome (FCMS) is a cortical-subcortical pseudobulbar palsy characterized by automatic voluntary dissociation of facio-masticatory-pharyngo-glosso-laryngeal movements. FCMS is typically caused by vascular insults on the bilateral anterior opercular or adjacent subcortical areas. Acute onset of FCMS secondary to a unilateral lesion is extremely rare. Herein we present a case of FCMS caused by acute unilateral anterior opercular infarction with preexisting bilateral leukoaraiosis. Our case shows that an acute unilateral anterior opercular lesion can decompensate preexisting corticobulbar-subcortical lesions and cause the typical features of FCMS.
福瓦-沙瓦尼-玛丽综合征（FCMS）是一种皮质-皮质下假性延髓麻痹，其特征为面-咀嚼-咽-舌-喉运动的自动随意分离。FCMS通常由双侧前岛盖或相邻皮质下区域的血管损伤引起。继发于单侧病变的FCMS急性发作极为罕见。在此，我们报告一例由急性单侧前岛盖梗死伴双侧脑白质疏松症引起的FCMS病例。我们的病例表明，急性单侧前岛盖病变可使先前存在的皮质延髓束-皮质下病变失代偿，并导致FCMS的典型特征。
