Bopp C, Peres M, Kosminski B, Azambuja M, Bakos L
Med Cutan Ibero Lat Am. 1975;3(2):149-59.
Two cases of Porphyria cutanea tarda with sclerodermoid changes associated with cataracta are studied. Far from being considered as an authentic scleroderma, the sclerodermoid aspect, very common in patients with Porphyria cutanea tarda, seems to represent one among the many residual alterations of the precocious cutaneous senescence, peculiar to these individuals hypersensitive to luminic radiations. The first patient had familial cases of cataracta. The second had no familial occurrence of it. The association of cataracta and Porphyria cutanea tarda, for the first time mentioned in the literature, would be one complication to be added to this very polymorphous syndrome.
对两例迟发性皮肤卟啉病伴有硬皮病样改变并合并白内障的病例进行了研究。迟发性皮肤卟啉病患者中非常常见的硬皮病样表现,远非被视为真正的硬皮病,似乎是这些对光辐射敏感个体早熟皮肤衰老的众多残留改变之一。第一例患者有白内障家族史。第二例患者无家族性白内障病史。文献中首次提及的白内障与迟发性皮肤卟啉病的关联,将是这种非常多形性综合征的又一并发症。