Sarisozen B, Durak K, Ozturk C
Uludag University Faculty of Medicine, Department of Orthopedic Surgery, 16059 Bursa, Turkey.
Acta Orthop Belg. 2002 Oct;68(4):412-6.
Adamantinoma of the long bones is a rare, low-grade malignancy with a marked predilection for the tibia and is usually seen in patients during the second to fifth decades of life. Adamantinomas have also been reported in children, but the histological pattern in this age group is different from that seen in adults. We report a case of adamantinoma of the tibia in a 9-year-old boy. Histologically, the lesion was osteofibrous dysplasia with an epithelial component, called "differentiated adamantinoma". An osteofibrous dysplasia-like adamantinoma (differentiated adamantinoma) may be the precursor lesion of the classic type of adamantinoma.
长骨造釉细胞瘤是一种罕见的低度恶性肿瘤，显著好发于胫骨，常见于20至50岁的患者。也有儿童造釉细胞瘤的报道，但该年龄组的组织学模式与成人不同。我们报告一例9岁男孩的胫骨造釉细胞瘤。组织学上，病变为伴有上皮成分的骨纤维发育不良，称为“分化型造釉细胞瘤”。骨纤维发育不良样造釉细胞瘤（分化型造釉细胞瘤）可能是经典型造釉细胞瘤的前驱病变。
