[合并肺大疱的结节性肺淀粉样变性；病例报告]

[Nodular pulmonary amyloidosis with bullae; report of a case].

作者信息

Ishibashi H, Akamatsu H, Sunamori M, Ishibashi T, Iwata T

机构信息

Department of Cardiothoracic Surgery, Tokyo Medical and Dental University, Tokyo, Japan.

出版信息

Kyobu Geka. 2002 Nov;55(12):1069-72.

PMID:12428345

Abstract

A 53-year-old male was admitted to the hospital because of progressive paralysis of inferior limb. Chest X-ray film and chest computed tomography (CT) on admission showed a small nodule with bullae in the right lower lung field. After CT-guided marking, partial lung resection including the nodule was performed. The cut surface of the resected specimen showed a tumor (10 mm in diameter) in a bullae measuring 14 mm in diameter. The tumor was diagnosed as amyloidosis. Fourty-six cases of primary localized pulmonary amyloidosis were reported in Japan. However, primary localized pulmonary amyloidosis with bullae is extremely rare, only 3 cases have been reported.

摘要

一名53岁男性因下肢进行性麻痹入院。入院时胸部X线片和胸部计算机断层扫描（CT）显示右下肺野有一个伴有大疱的小结节。在CT引导下进行标记后，对包括结节在内的部分肺组织进行了切除。切除标本的切面显示在一个直径为14毫米的大疱内有一个肿瘤（直径10毫米）。该肿瘤被诊断为淀粉样变性。日本曾报道过46例原发性局限性肺淀粉样变性病例。然而，伴有大疱的原发性局限性肺淀粉样变性极为罕见，仅报道过3例。