Aloulou S, Merad-Boudia Z
Service d'oncologie médicale, Hôpital Tenon, 4 rue de la Chine 75020 Paris.
Presse Med. 2002 Oct 26;31(35):1653-6.
The adenoid cystic carcinoma or cylindroma of the nasopharynx is a rare tumour characterised by its slow progression, high risk of local recurrence and prolonged survival, even in the locally advanced and/or metastatic forms. Treatment is pluridisciplinary.
In a 30 year-old man consulting for right retroauricular pain, hypoacousia and epistaxis, diagnosis of a nasopharyngeal cylindroma was made in 1994. Treatment consisted first line surgery combined with loco-regional radiotherapy. Twenty-six months after complete remission had been obtained, a loco-regional relapse was revealed, combined with pulmonary metastases. The treatment combining radiotherapy, surgery and chemotherapy led to the stabilisation of the disease.
The adenoid cystic carcinoma of the nasopharynx a rare neoplasia of the head and neck, characterised by its slow progression over time, a high risk of relapse and the progression of metastases at distance. The corner stone of its therapeutic management is surgery. Radiotherapy improves the local control of the disease and chemotherapy is helpful in treating the metastatic disease.
鼻咽腺样囊性癌或圆柱瘤是一种罕见肿瘤，其特点是进展缓慢、局部复发风险高、生存期长，即使是局部晚期和/或转移型也是如此。治疗是多学科的。
一名30岁男性因右耳后疼痛、听力减退和鼻出血前来就诊，1994年诊断为鼻咽圆柱瘤。一线治疗为手术联合局部区域放疗。在获得完全缓解26个月后，发现局部区域复发并伴有肺转移。放疗、手术和化疗联合治疗使病情稳定。
鼻咽腺样囊性癌是一种罕见的头颈部肿瘤，其特点是随时间进展缓慢、复发风险高以及远处转移进展。其治疗管理的基石是手术。放疗可改善疾病的局部控制，化疗有助于治疗转移性疾病。
