Hachi H, Othmany A, Douayri A, Bouchikhi C, Tijami F, Laâlou L, Chami M, Boughtab A, Jalil A, Benjelloun S, Ahyoud F, Kettani F, Souadka A
Service de chirurgie carcinologique, institut national d'oncologie Sidi Mohamed Ben Abdellah, Rabat, Maroc.
Gynecol Obstet Fertil. 2002 Sep;30(9):692-5. doi: 10.1016/s1297-9589(02)00416-2.
The authors report a rare case of the ovarian juvenile granulosa cell tumor associated with Maffucci's syndrome (enchondromathosis + hemangiomas), no heriditary mesodermal dysplasia. Sarcomatous changes of chondromas are encountered most frequently; however other various typed neoplasma have been reported: ovarian juvenile granulosa cell tumor may occur not infrequently in female patients with Maffucci's syndrome in the first or second decades. Sarcomatous changes of choromas established prognosis of the Maffucci's syndrome.
作者报告了一例罕见的卵巢幼年型颗粒细胞瘤，其与马富西综合征（内生软骨瘤病 + 血管瘤）相关，无遗传性中胚层发育异常。软骨瘤的肉瘤样变最为常见；然而，也有其他各种类型的肿瘤被报道：卵巢幼年型颗粒细胞瘤在患有马富西综合征的女性患者的第一个或第二个十年中可能并不少见。软骨瘤的肉瘤样变决定了马富西综合征的预后。
