Christman J E, Ballon S C
David Grant USAF Medical Center, Travis Air Force Base, California 94535.
Gynecol Oncol. 1990 May;37(2):290-1. doi: 10.1016/0090-8258(90)90350-t.
Maffucci's syndrome, a congenital condition of generalized mesodermal dysplasia, is most often associated with multiple enchondromas and soft tissue hemangiomas or lymphangiomas. This case report describes the development of an unusual ovarian fibrosarcoma and subsequent ovarian adenofibroma in a young woman with the syndrome. The importance of aggressive surveillance in this and similar orthopedic syndromes is stressed.
马富西综合征是一种全身性中胚层发育异常的先天性疾病，最常与多发性内生软骨瘤以及软组织血管瘤或淋巴管瘤相关。本病例报告描述了一名患有该综合征的年轻女性发生罕见的卵巢纤维肉瘤及随后的卵巢腺纤维瘤的情况。强调了对该疾病及类似骨科综合征进行积极监测的重要性。
