先天性孤立性肠纤维瘤病

Congenital solitary intestinal fibromatosis.

作者信息

Numanoglu A, Davies J, Millar A J W, Rode H

机构信息

Department of Paediatric Surgery, Red Cross War Memorial Children's Hospital, University of Cape Town, Rondebosch, Cape Town, South Africa.

出版信息

Eur J Pediatr Surg. 2002 Oct;12(5):337-40. doi: 10.1055/s-2002-35957.

DOI:10.1055/s-2002-35957

PMID:12469263

Abstract

Neonatal intestinal obstruction due to a tumour is rare. We report a six-day-old male neonate who presented with abdominal distension and vomiting. Laparotomy revealed colonic obstruction caused by a stenosing fibrotic lesion in the proximal transverse colon. Histopathological examination of the resected specimen confirmed fibromatosis. We believe this represents the third reported case of solitary colonic fibromatosis. The literature on neonatal intestinal fibromatosis is reviewed.

摘要

新生儿因肿瘤导致的肠梗阻较为罕见。我们报告一例6日龄男性新生儿，表现为腹胀和呕吐。剖腹探查发现近端横结肠有一狭窄性纤维化病变导致结肠梗阻。切除标本的组织病理学检查证实为纤维瘤病。我们认为这是第三例报告的孤立性结肠纤维瘤病。本文对新生儿肠道纤维瘤病的文献进行了综述。