Depreter M, Vandesompele J, Espeel M, Speleman F, Roels F
Department of Human Anatomy, Embryology, Histology and Medical Physics, Ghent University, Godshuizenlaan 4, B-9000 Ghent, Belgium.
J Endocrinol. 2002 Dec;175(3):779-92. doi: 10.1677/joe.0.1750779.
Peroxisomes are ubiquitous organelles required for several metabolic functions. Their dysfunction is responsible for a group of human inherited disorders. In the search for endogenous factors regulating the peroxisomal compartment in normal liver, we treated female rats with dehydroepiandrosterone (DHEA) and 25-hydroxycholecalciferol for 1 and 6 days. Relative transcription levels of 39 selected genes were evaluated by real-time quantitative RT-PCR analysis. Catalase (peroxisomal marker)-specific activity was assayed in total liver homogenate and peroxisomes were visualized by catalase localization. DHEA induced peroxisome proliferation and raised catalase specific activity. Expression levels of 16 (of which 11 were peroxisomal) genes were altered. Pex 11, acyl-CoA oxidase,l - andd -multifunctional enzyme, thiolase 1, phytanoyl-CoA hydroxylase, 70 kDa peroxisomal membrane protein and very long chain acyl-CoA synthetase were upregulated, three others were downregulated. Vitamin D caused downregulation of six genes. Administration of vitamin D to peroxisomal disorder patients may be contraindicated. The adrenocortical hormone DHEA is a potential natural regulator of the peroxisomal compartment. Its therapeutic use in X-linked adrenoleukodystrophy, some other beta-oxidation defects and classical Refsum should be considered.
过氧化物酶体是多种代谢功能所必需的普遍存在的细胞器。它们的功能障碍导致了一组人类遗传性疾病。在寻找正常肝脏中调节过氧化物酶体区室的内源性因子的过程中,我们用脱氢表雄酮(DHEA)和25-羟基胆钙化醇处理雌性大鼠1天和6天。通过实时定量RT-PCR分析评估39个选定基因的相对转录水平。在全肝匀浆中测定过氧化氢酶(过氧化物酶体标志物)的特异性活性,并通过过氧化氢酶定位观察过氧化物酶体。DHEA诱导过氧化物酶体增殖并提高过氧化氢酶特异性活性。16个基因(其中11个是过氧化物酶体基因)的表达水平发生了改变。Pex 11、酰基辅酶A氧化酶、l-和d-多功能酶、硫解酶1、植烷酰辅酶A羟化酶、70 kDa过氧化物酶体膜蛋白和极长链酰基辅酶A合成酶上调,另外三个下调。维生素D导致六个基因下调。对过氧化物酶体疾病患者使用维生素D可能是禁忌的。肾上腺皮质激素DHEA是过氧化物酶体区室的一种潜在天然调节剂。应考虑其在X连锁肾上腺脑白质营养不良、其他一些β氧化缺陷和经典型Refsum病中的治疗用途。