Shintani Yasushi, Ohta Mitsunori, Hazama Kenji, Minami Masato, Okumura Meinoshin, Hirabayashi Hirohisa, Matsuda Hikaru
Department of Surgery, E1, Osaka University Graduate School of Medicine, 2-2 Yamadaoka, Suita, Osaka 565-0871, Japan.
Surg Today. 2002;32(12):1068-71. doi: 10.1007/s005950200215.
A 19-year-old woman with von Recklinghausen's disease was admitted with symptoms of hoarseness. A computed tomography scan showed a bilateral cervicomediastinal tumor. An extirpation of the left cervicomediastinal tumor was performed for the purpose of diagnosis and treatment. On thoracotomy, the tumor, which measured 9 x 8 x 4 cm in size, arose from the intrathoracic vagal nerve and the left tumor was resected with a segment of the vagal nerve and recurrent nerve. The pathological diagnosis of the tumor was a neurofibroma. The tumor on the right side was left untreated due to concerns about possibly causing palsy of the bilateral recurrent nerve and also because of the asymptomatic state of the right tumor. Mediastinal neurofibroma in a patient with von Recklinghausen's disease often arises from the intrathoracic vagal nerve. To our knowledge, this is the first report of bilateral cervicomediastinal neurofibroma originating from the vagal nerves.
一名患有冯雷克林霍增氏病的19岁女性因声音嘶哑症状入院。计算机断层扫描显示双侧颈纵隔肿瘤。为了诊断和治疗，对左侧颈纵隔肿瘤进行了切除。开胸手术时，肿瘤大小为9×8×4厘米，起源于胸段迷走神经，左侧肿瘤与一段迷走神经和喉返神经一并切除。肿瘤的病理诊断为神经纤维瘤。由于担心可能导致双侧喉返神经麻痹，且右侧肿瘤无症状，右侧肿瘤未予治疗。冯雷克林霍增氏病患者的纵隔神经纤维瘤常起源于胸段迷走神经。据我们所知，这是首例起源于迷走神经的双侧颈纵隔神经纤维瘤报告。
