White R J, Bass S P
Department of Anaesthesia, Addenbrooke's Hospital, Hills Road, Cambridge CB2 2QQ, UK.
Paediatr Anaesth. 2003 Feb;13(2):94-102. doi: 10.1046/j.1460-9592.2003.00889.x.
Myotonic dystrophy is a neuromuscular condition inherited in an autosomal dominant fashion, and is most commonly diagnosed in the neonatal period. With improving levels of care, these patients are now presenting more commonly for anaesthesia. We review the clinical features of the condition, and then discuss the steps in the anaesthetic process, outlining the anaesthetic implications of myotonic dystrophy at each stage.
强直性肌营养不良症是一种以常染色体显性方式遗传的神经肌肉疾病，最常在新生儿期被诊断出来。随着护理水平的提高，这些患者现在更常接受麻醉。我们回顾了该疾病的临床特征，然后讨论麻醉过程中的步骤，概述强直性肌营养不良症在每个阶段的麻醉影响。
