Watkins Robert G, Reynolds Richard A K, McComb J Gordon, Tolo Vernon T
Department of Orthopedics, University of Southern California, Los Angeles 90033, USA.
Spine (Phila Pa 1976). 2003 Feb 1;28(3):E45-50. doi: 10.1097/01.BRS.0000042235.41817.04.
Two cases of lymphangiomatosis of the spine are presented.
To report two cases of lymphangiomatosis of the spine requiring surgical intervention and to review the literature.
Lymphangiomatosis is a rare childhood disease characterized by abnormal lymph tissue at multiple sites. Skeletal and visceral involvement are both common. Prognosis depends on the extent of extraskeletal disease.
Two cases of lymphangiomatosis causing neural compression and instability at the cervicothoracic junction are presented. Both patients underwent surgical decompression and stabilization.
One patient died, whereas the other regained full function and activity.
Surgery is indicated when lymphangiomatosis causes neural compression and instability of the spine. Surgical outcome is strongly influenced by extraskeletal involvement.
报告两例脊柱淋巴管瘤病病例。
报告两例需要手术干预的脊柱淋巴管瘤病病例并复习相关文献。
淋巴管瘤病是一种罕见的儿童疾病，其特征为多个部位的淋巴组织异常。骨骼和内脏受累均较为常见。预后取决于骨骼外疾病的范围。
报告两例导致颈胸交界处神经受压和不稳定的淋巴管瘤病病例。两名患者均接受了手术减压和稳定治疗。
一名患者死亡，而另一名患者恢复了全部功能和活动能力。
当淋巴管瘤病导致神经受压和脊柱不稳定时，应进行手术治疗。手术结果受骨骼外受累情况的影响很大。
