López Gutiérrez J C, Ros Z, Martínez L, Díaz M, Leal N, Rivas S, Hernández F
Unidad de Cirugía Plástica Pediátrica, Hospital Infantil La Paz, Paseo de la Castellana, 261, 28046 Madrid.
Cir Pediatr. 2002 Oct;15(4):145-7.
Unlike hemangiomas and low-flow vascular malformations which are very common in children, arterial anomalies have small incidence. Differential diagnosis is difficult, and needs a physician familiarized with vascular anomalies. Appropriate treatment must be planned by multidisciplinary team considering the patient's age, and anatomical location. Twenty-eight children with high flow vascular malformations have been treated since 1990 at La Paz Children's Hospital Vascular Anomalies Program. We excluded of the study group patients with central nervous system lesions. 85% of the patients had malformation in stage I or II (according the ISSVA accepted Schöbinger stating) and most of them were erroneously diagnosed as hemangioms with a variety of inappropriate treatments previously performed. Doppler Ultrasound and Magnetic Resonance confirmed malformation flow and extension. Angiography and selective embolization was only considered as therapeutic approach in candidates to surgical resection. 16 patients underwent complete resection of the malformation including one foot and two fingers amputation and five more incomplete resection of the ulcerate area. In conclusion, we did not find age at onset, sex and symptoms relationship. Laser, radiotherapy, surgical ligation or partial resection must be considered inappropriate therapies which may stimulate AVM exacerbation. Only radical surgical procedure after selective endovascular embolization will be successful but then reconstructive surgery should be performed to achieve good aesthetic and functional results.
与在儿童中非常常见的血管瘤和低流量血管畸形不同,动脉畸形的发病率很低。鉴别诊断困难,需要熟悉血管畸形的医生来进行。必须由多学科团队根据患者的年龄和解剖位置制定合适的治疗方案。自1990年以来,拉巴斯儿童医院血管畸形项目已治疗了28例高流量血管畸形患儿。我们将有中枢神经系统病变的患者排除在研究组之外。85%的患者处于I期或II期畸形(根据国际血管畸形研究学会认可的施宾格分期),其中大多数之前被错误诊断为血管瘤,并接受了各种不恰当的治疗。多普勒超声和磁共振成像确定了畸形的血流情况和范围。血管造影和选择性栓塞仅被视为手术切除候选者的治疗方法。16例患者接受了畸形的完整切除,其中包括1例足部和2例手指截肢,另有5例对溃疡区域进行了不完全切除。总之,我们未发现发病年龄、性别与症状之间的关系。激光、放疗、手术结扎或部分切除被认为是不恰当的治疗方法,可能会刺激动静脉畸形加重。只有在选择性血管内栓塞后进行根治性手术才会成功,但随后应进行重建手术以获得良好的美学和功能效果。