Yan Ju, Whittom Renaud, Delage Robert, Drouin Régen
Department of Medical Biology, Division of Pathology, Laval University, Québec, PQ, Canada.
Cancer Genet Cytogenet. 2003 Jan 15;140(2):138-44. doi: 10.1016/s0165-4608(02)00682-9.
In a young female patient presenting with a myelodysplastic syndrome (MDS), a unique clone involving six structural chromosome rearrangements was identified using G-banding and molecular cytogenetic techniques. Fifty GTG-banded metaphases from bone marrow were initially analyzed and all metaphases contained all of the six structural chromosome rearrangements. To further define the GTG-banded karyotype, a series of fluorescence in situ hybridization and primed in situ labeling experiments were performed and the karyotype was then characterized as: 46,XX,r(5)(p13q13),der(20)t(5;20),dup(11)(p11.2p15), r(11)(p15q25),del(13)(q14),idic(22)(p11). The patient quickly progressed to acute nonlymphocytic leukemia three months after the diagnosis and died of a hemorrhage in the brain parenchyma two months later. In this case, the multiple structural chromosome rearrangements conferred an obvious cellular proliferative advantage and indicated a very poor prognosis. Considering that multiple chromosome abnormalities associated with MDS transformation are often polyclonal, this unique clone involving six structural chromosome rearrangements make our case highly unusual.
在一名患有骨髓增生异常综合征(MDS)的年轻女性患者中,使用G显带和分子细胞遗传学技术鉴定出一个涉及六种结构染色体重排的独特克隆。最初分析了来自骨髓的50个G显带中期细胞,所有中期细胞都包含所有六种结构染色体重排。为了进一步确定G显带核型,进行了一系列荧光原位杂交和引物原位标记实验,核型随后被确定为:46,XX,r(5)(p13q13),der(20)t(5;20),dup(11)(p11.2p15), r(11)(p15q25),del(13)(q14),idic(22)(p11)。该患者在诊断后三个月迅速进展为急性非淋巴细胞白血病,两个月后死于脑实质出血。在这种情况下,多种结构染色体重排赋予了明显的细胞增殖优势,并表明预后非常差。考虑到与MDS转化相关的多种染色体异常通常是多克隆的,这个涉及六种结构染色体重排的独特克隆使我们的病例非常罕见。