Mahdhaoui A, Bouraoui H, Tabarki B, Majdoub M, Trimeche B, Mahdhaoui N, Chabrak S, Ernez-Hajri S, Jeridi G, Ammar H
Service de cardiologie, hôpital Farhat Hached, avenue Ibn El Jazar, 4000 Sousse, Tunisie.
Acta Clin Belg. 2003 Jan-Feb;58(1):54-7. doi: 10.1179/acb.2003.58.1.008.
Familial hypertrophic cardiomyopathy (HCM) with Wolff-Parkinson-White (WPW) syndrome is extremely rare and associated with a high risk of ventricular tachyarrhythmia and sudden death. We report a familial form of hypertrophic cardiomyopathy associated with Wolff-Parkinson-White syndrome in two siblings 7 and 12-year-old. These patients showed progression to left ventricular dilatation. Early recognition and treatment of such forms can improve such evolution and the risk of sudden death.
伴有 Wolff-Parkinson-White（WPW）综合征的家族性肥厚型心肌病（HCM）极为罕见，且与室性快速心律失常和猝死的高风险相关。我们报告了一例发生在两名7岁和12岁兄弟姐妹身上的与Wolff-Parkinson-White综合征相关的家族性肥厚型心肌病。这些患者出现了左心室扩张。对此类病症的早期识别和治疗可改善这种病情发展及猝死风险。
