Niiyama Yukitoshi, Kanaya Noriaki, Namiki Akiyoshi
Department of Anesthesiology, Sapporo Medical University, School of Medicine, Sapporo 060-8556.
Masui. 2003 May;52(5):524-6.
A 50-year-old woman was scheduled for laparoscopic cholecystectomy under general anesthesia. She was suffering from Charcot-Marie-Tooth (CMT) disease for 21 years, and implanted with a permanent pacemaker for IIIrd degree AV block. Anesthesia was induced with fentanyl and propofol, and maintained with oxygen-air-sevoflurane. Neuromuscular blockade was not used because of the presence of peripheral neuropathy and respiratory muscle weakness. We suggest that sevoflurane anesthesia might be useful for anesthetic management of CMT patient with a risk of postoperative respiratory failure.
一名50岁女性计划在全身麻醉下进行腹腔镜胆囊切除术。她患夏科-马里-图斯（CMT）病21年，因三度房室传导阻滞植入了永久性起搏器。麻醉诱导使用芬太尼和丙泊酚，维持使用氧气-空气-七氟醚。由于存在周围神经病变和呼吸肌无力，未使用神经肌肉阻滞剂。我们建议，七氟醚麻醉可能有助于对有术后呼吸衰竭风险的CMT患者进行麻醉管理。
