骨盆恶性颗粒细胞瘤的罕见表现：病例报告及文献复习
Unusual presentation of a malignant granular cell tumor of the pelvis: case report and literature review.
作者信息
Berg Jena C, Tewari Krishnansu S, Del Rosario Raul, Berman Michael L
机构信息
UCI College of Medicine, University of California, Irvine, Medical Education Bldg 802, Irvine, CA 92697, USA.
出版信息
Gynecol Oncol. 2003 Jul;90(1):224-30. doi: 10.1016/s0090-8258(03)00172-0.
BACKGROUND
Malignant granular cell tumors are among the rarest of soft tissue cancers, currently understood to be of Schwann cell origin. As with their benign counterparts, malignant granular cell tumors (MGCTs) have a wide anatomic distribution and carry a poor prognosis, with recurrence and metastasis typically within 1 year of diagnosis. Only a handful of MGCTs have been described in the pelvis.
CASE
We describe a case of malignant granular cell tumor that presented as a pararectal mass associated with severe rectal pain. The patient underwent pelvic exenteration and postoperative radiation therapy. She recurred with evidence of liver metastases on imaging studies 8 months following her exenteration.
CONCLUSION
We discuss the diagnosis and prognosis of malignant granular cell tumors arising in the pelvis.
背景
恶性颗粒细胞瘤是最罕见的软组织癌之一，目前认为起源于施万细胞。与良性颗粒细胞瘤一样，恶性颗粒细胞瘤（MGCTs）具有广泛的解剖分布，预后较差，通常在诊断后1年内复发和转移。骨盆中仅报道过少数几例MGCTs。
病例
我们报告一例恶性颗粒细胞瘤，表现为直肠旁肿块并伴有严重的直肠疼痛。患者接受了盆腔脏器清除术及术后放射治疗。盆腔脏器清除术后8个月，影像学检查显示她出现了肝转移复发。
结论
我们讨论了骨盆中发生的恶性颗粒细胞瘤的诊断和预后。
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